The genetic spectrum of arNSHL in Chinese patients mainly includes mutations in GJB2, SLC26A4, MYO7A, POU3F4, USH2A and TMC1. Mutations in GJB2, followed by mutations in SLC26A4, are the most commonly identified cause of sensorineural hearing loss in Chinese patients [2]. Here, TMC1 is linked to sensorineural hearing loss disorder.