Drosophila Ter94 has been widely studied as a disease model of inclusion body myopathy with early-onset Paget disease and frontotemporal dementia (IBMPFD) [35], [36], a model of interaction with retinal pathology caused by misfolded rhodopsin [37], and one of interaction with polyglutamine (polyQ) disease caused by expression of expanded polyQ [38]. The gene discussed is RHO; the disease is frontotemporal dementia.