The 5-year survival of treated AAV is over 70%, but relapse rate remains relatively high.14–17 A systematic review by the European League Against Rheumatism systemic vasculitis task force16 has revealed that the 5-year survival for GPA, MPA, and EGPA was 74% to 91%, 45% to 76%, and 60% to 97%, respectively. Here, GYPA is linked to necrotizing vasculitis.