WT1 and desmoplastic small round cell tumor: Desmoplastic small round cell tumor (DSRCT) is a highly aggressive, rare tumor of mesenchymal origin whose oncogenic effect is presumed to originate from the unique chromosomal translocation t(11;22)(p13:q12) [1, 2], leading to the fusion of the N-terminal domain of Ewing's sarcoma gene EWS, to the C-terminal domain of Wilms' tumor suppressor gene, WT1, which is found in most but not all DSRCTs [3].