In particular, from the prognostic perspective, we can expect successful results of CI in hereditary deafness with mutation of specific genes, such as, GJB2, SLC26A4, mitochondrial mutations, OTOF, Usher syndrome type I, DFNA9 (COCH), and DFNA17 (MYH9) [6]. The gene discussed is MYH9; the disease is Usher syndrome type 1.