Stargardt macular dystrophy (STGD) is the most common form of juvenile-onset macular degeneration; it is inherited as an autosomal-recessive trait and caused by mutations in the ABCA4 gene.1–3 Most cases present with central visual loss in early teenage years and ophthalmoscopy classically reveals macular atrophy with yellowish-white flecks at the posterior pole at the level of the retinal pigment epithelium (RPE).1 This evidence concerns the gene ABCA4 and severe early-childhood-onset retinal dystrophy.