USH2A and deafness: In addition, mutations in MYO7A, USH1C, DFNB31, CIB2, CDH23 and PCDH15 were also reported in non-syndromic deafness without retinal degeneration [22], [23] and mutations in USH2A and CLRN1 have been reported in patients with isolated RP or retinal dystrophies and no deafness [24]–[26].