KCNJ11 and hyperinsulinism: It is well established that the potassium inwardly rectifying channel, subfamily J, member 11 (KCNJ11) gene located at chromosome 11p15.1 is involved in insulin secretion in humans and that mutations in this KCNJ11 gene can cause congenital hyperinsulinism [4] and permanent neonatal diabetes [5].