USH2A and nodular sclerosis classical Hodgkin lymphoma: Despite its wide expression, defects in usherin have only been linked with Usher syndrome type 2 (USH2; MIM: 276901) [11], [12], [13], [14], nonsyndromic RP [15], and nonsyndromic hearing loss (NSHL) [16], implying its special role in maintaining the function of the capillary and structural basement membranes of the two ciliated sensory neurons, namely photoreceptor cells and cochlear hair cells.