Although these patients did not bear any PSTPIP1 mutations, they presented CCTG microsatellites repetitions in the promoter region of the PSTPIP1 gene; this condition, characterized by the triad of pyoderma gangrenosum, acne, and hidradenitis suppurativa, has been distinguished from the “classic” PAPAs and identified with the acronym PASH (pyoderma gangrenosum, acne, and suppurativa hidradenitis) syndrome [119]. This evidence concerns the gene PSTPIP1 and pyoderma gangrenosum.