SMARCB1 is known to be disrupted in malignant rhabdoid tumors, round cell soft-tissue sarcomas (most were a subset of tumors resembling extraskeletal myxoid chondrosarcoma with rhabdoid features, epithelioid sarcomas, and schwannomatosis [34]–[38]. The gene discussed is SMARCB1; the disease is myxoid chondrosarcoma.