Cystic Fibrosis is a lethal genetic disease (Davis et al., 1996; Lyczak et al., 2002) in which mutations in the CF transmembrane Conductance Regulator (CFTR) gene result in defective function and/or processing of the mutant protein CFTR (Zielenski and Tsui, 1995; Gadsby et al., 2006). The gene discussed is CFTR; the disease is cystic fibrosis.