Carnitine Palmitoyltransferase 2 (CPT2) and Very Long Chain AcylCoA Dehydrogenase (VLCAD) deficiencies belong to a group of more than fifteen genetic diseases affecting one of the enzymes of the mitochondrial ß-oxidation pathway, well characterized at the clinical and molecular levels, but for which treatments remain quite limited [11,12]. The gene discussed is CPT2; the disease is hereditary disease.