PJVK and hearing loss disorder: The results of gene expression analysis of each cochlear turn showed that 4 ADNSHL genes (Pou4f3, Slc17a8, Tmc1, and Crym) and 9 autosomal recessive non syndromic hearing loss genes (Otof, Strc, Ush1c, Pcdh15, Grxcr1, Dfnb59, Slc26a5, Lhfpl5, and Ptprq) were changed 2-fold or more (Table 2).