Mutations in TMPRSS3 (transmembrane serine protease 3) [3], TMC1 (transmembrane cochlear-expressed gene 1) [4], USHIC (Usher 1C) [5], CDH23 (cadherin 23) [6] and TMIE (transmembrane inner ear) [7] are known to play a causative role in NSHL. Here, TMPRSS3 is linked to nodular sclerosis classical Hodgkin lymphoma.