SMARCB1 and extraskeletal myxoid chondrosarcoma: For instance, homozygous deletions of the SNF5 locus 22q11.2 are found in small-cell hepatoblastomas and poorly differentiated chordomas [44], [45] and inactivating mutations and/or deletion of SNF5 are observed in extraskeletal myxoid chondrosarcomas [46], undifferentiated sarcomas [47], epitheliod sarcomas [48] and meningiomas [41], [49].