After adjusting for potential confounders, MBL deficiency (<0.5 μg/ml) was found less frequently in cases than controls (26 vs. 41%, OR 0.4, 95% confidence interval (CI) 0.20-0.95, p=0.04) as were low producing MBL genotypes (11 vs. 23%, OR 0.2, 95% CI 0.08-0.75, p=0.01), whereas NOD2 polymorphisms were similarly distributed. Here, NOD2 is linked to hyperinsulinemic hypoglycemia, familial, 4.