It is difficult to differentiate the diagnosis from histologically dissimilar lesions that include glomangioma, myopericytoma and angioleiomyoma and differential diagnosis with pleomorphic adenoma of parotid gland, neurinoma, Adenoid Cystic Carcinoma and tumor derived from the meninges et al. In our case, the glomus like cells were arranged in a concentric perivascular array with vimentin, SMA, MSA, CD99, S-100, Bcl-2 positivity and CD31, CD34, CK9, EMA, HMB45, Melan A negativity, which are the histological characteristics of glomangiopericytoma. The gene discussed is CD99; the disease is schwannoma.