RBFOX3 and Huntington disease: Indeed, in agreement with other studies [30], [31], our results confirmed the presence of striatal neuronal loss in R6/2 transgenic mouse model of HD, revealed by a difference for the number of NeuN positive neurons between various experimental groups (F3,17 = 7.30, p = 0.002) [R6/2: intact (n = 5), GFP- (n = 4), pENK (n = 6); WT: (n = 6)].