These included 20 patients with CAPS (14 with the chronic, inflammatory, neurologic, cutaneous and articular (CINCA) syndrome / neonatal onset multisystem inflammatory disease (NOMID) and 6 with Muckle-Wells syndrome), mevalonate kinase deficiency (n = 3), TNF-receptor associated periodic syndromes (n = 2), familial mediterranean fever (n = 1) and patients with genetically undetermined autoinflammatory conditions. Here, MVK is linked to Muckle-Wells syndrome.