In Chianina cattle, a missense mutation in exon 6 (c.491G > A) of the bovine ATP2A1/SERCA1 gene, was implicated in Congenital Pseudomyotonia [24,25], a disease very similar to BSP and paralleled to human Brody disease by Drögemüller and collaborators, [26]. Here, ATP2A1 is linked to Brody myopathy.