As shown in Table 1, some of these rodent models display both autism-like behavior and cerebellar pathology including the FMR1 knockout (KO) mouse, the engrailed homeobox 2 (EN2) KO mouse, and the staggerer mouse (Goldowitz and Koch, 1986; Petit et al., 1995; Lalonde et al., 1996; Kuemerle et al., 1997; Doulazmi et al., 2001; Rogers et al., 2001; Ellegood et al., 2010). This evidence concerns the gene EN2 and autism.