Although various histopathological lesions have been reported in ADPKD patients, including focal segmental glomerulosclerosis (FSGS), membranous nephropathy, minimal change disease, and immunoglobulin A (IgA) nephropathy [4-18], myeloperoxidase (MPO)-antineutrophil cytoplasmic antibody (ANCA)-associated crescentic glomerulonephritis (CrGN) has not been reported so far. This evidence concerns the gene MPO and focal segmental glomerulosclerosis.