Ataxia-telangiectasia (A-T, ATM mutation), the related A-T like disease (ATLD, MRE11 mutation), Nijmegen breakage syndrome (NBS, NBS1/NBN mutation) and the more recently identified NBS like disease (NBSLD, RAD50 mutation), all present with similar pathological outcomes in humans (Stracker and Petrini, 2011). Here, NBN is linked to Ataxia-telangiectasia.