Several members of the myosin gene family have been implicated in hearing loss, including MYO7A, where mutations in humans are responsible for causing non-syndromic dominant (DFNA11; [8], [9]) and recessive (DFNB2; [10], [11]) deafness and the deaf-blindness condition Usher Syndrome type 1B (USH1B; [12]–[14]). The gene discussed is MYO7A; the disease is Usher syndrome type 1B.