RAG1 and Omenn syndrome: A similar frame shift mutations like in the LEW/Ztm-Rag1em1Ztm were observed in the human Rag1 gene in two patients with Omenn’s syndrome carrying an adenosine deletion at position 877 of the Rag1 cDNA also introducing a premature stop codon in front of the nonamer binding region (NBR) [49,50].