aPL-related chorea is common in children and it is important to exclude other possible causes, such as Sydenham’s chorea, benign hereditary chorea, DNA repair diseases (ataxia-telangiectasia, ataxia with oculomotor apraxia type 1 and 2), Wilson’s disease, pantothenate kinase-associated neurodegeneration (Walker, 2011). This evidence concerns the gene PANK1 and Benign familial chorea.