VEGFA and Hermansky-Pudlak syndrome: In contrast to PEF and PBMC samples, we found low-plasma VEGF levels in severe HPS cases during the first 3 days of hospitalization (n = 15, mean 30.4 ± 8.1), and an increase in plasma VEGF levels during recovery (n = 17, mean 212 ± 49.7; P = 0.001) (Figures 3(a), and 3(b); Table 1).