Although first described in 1961 as a case of pancreatitis with autoimmune features [9], the term AIP was first used to describe a case involving diffuse enlargement of the pancreas, irregular narrowing of the pancreatic duct and serological markers of hyper-γ-globulinaemia, as well as antinuclear antibody (ANA) positivity by indirect immunofluorescence (IIF) [10]. The gene discussed is BTG3; the disease is autoimmune pancreatitis.