Although patients showing a fibrillar pattern of IgA deposits typically have other clinical findings consistent with DH, it has been suggested that those patients may have a higher incidence of atypical features, such as urticarial or psoriasiform skin lesions, the absence of GSD, or an HLA-B8/DR3/DQ2 haplotype [3]. The gene discussed is CD79A; the disease is disorder of glycogen metabolism.