MODY is not a single entity as at least twelve MODY subtypes with distinct genetic aetiologies have been reported in the literature: MODY1-HNF4A, MODY2-GCK, MODY3-HNF1A, MODY4-PDX1, MODY5-HNF1B, MODY6-NEUROD1, MODY7-KLF11, MODY8-CEL, MODY9-PAX4, MODY10-INS, MODY11-BLK and very recently MODY12-ABCC8[1], [2], [3]. Here, PAX4 is linked to MODY.