TLR4 and Miyoshi myopathy: Combined carriership of TLR2+2477 GG WT and TLR4+896 AG mutant alleles significantly increases the risk to develop hearing loss in BM (p<0.0001, OR 5.7, 95% CI 2.3–14.4, in MM patients: p  = 0.0001, OR 7.6, 95% CI 2.3–24, in PM patients: p  = 0.03, OR 13.9, 95% CI 1.3–147).