GABRA1 and autosomal dominant epilepsy with auditory features: These include the generalized Juvenile Myoclonic Epilepsy (JME) (to date with mutations in the EFHC1 or GABRA1 genes; penetrance ∼50%) [6], [7] and the focal-onset Autosomal Dominant Lateral Temporal Lobe Epilepsy (ADLTE) (also called Autosomal Dominant Partial Epilepsy with Auditory Features) with mutations in the LGI1 gene [8] (penetrance 67%) [9].