This diagnosis was also appropriate given the lack of autopsy findings indicative of hereditary spinocerebellar degeneration such as SCA3 and SCA6 and multiple system atrophy, and because several types of autoantibodies [9] were found that have been reported previously in association with autoimmune cerebellar ataxia, including anti-gliadin antibody. Here, ATXN3 is linked to multiple system atrophy.