Myosin VIIA has been implicated in recessively inherited Usher syndrome type 1B (USH1B) [8], atypical Usher syndrome (USH3) [9], nonsyndromic recessive (Deafness, Neurosensory, Autosomal Recessive 2 [DFNB2]) [10], and dominant (DFNA11) [11] hearing loss (HL). This evidence concerns the gene MYO7A and Usher syndrome type 1B.