Trauma, hormonal changes and infections (HTLV or HHV 8) have been suggested to play a role in the pathogenesis.4 Association of ALHE with nephrotic syndrome and pregnancy have been described.4, 5 Over-expression of estrogen and progesterone receptors was detected in pregnant women.6 Interleukin 5 and vascular endothelial growth factor were also found to be increased in some cases.7 Since they share many clinical and histopathological similarities, ALHE should be differentiated from Kimura's disease. Here, PGR is linked to nephrotic syndrome.