Levels of serum markers did not show any significant differences between IP patients with and without P. jirovecii colonization on oral corticosteroid therapy with respect to KL-6 (1370 ± 810.4 vs. 1030.6 ± 594.6), SP-A (86.6 ± 32.8 vs. 73.5 ± 44.5), SP-D (142.8 ± 145.1 vs. 102.3 ± 121.9), and β-D-glucan (both groups were under the detection limit) (Figs. 2e, f, g and 2h). Here, SFTPD is linked to incontinentia pigmenti.