Familial ARVD is primarily autosomal dominant, with several sub-types identified and mapped to distinct genetic loci to date – ARVD1 (14q24.3) [7], ARVD2 (1q42) [8], ARVD3 (14q11-q12) [9], ARVD4 (2q32) [10], ARVD5 (3p23) [11], ARVD6 (10p12-p14) [12], ARVD7 (10q22) [13], ARVD8 (6p24) [14], ARVD9 (12p11) [6], ARVD10 (8q12) and ARVD11 (18q21) [15]. The gene discussed is PKP2; the disease is Arrhythmogenic right ventricular dysplasia.