Genetic studies revealed that all cases of DSRCT harbor the t(11;22)(p13;q12) translocation, leading to a fusion of the N-terminal domain (NTD) of Ewing's sarcoma gene (EWS) to the C-terminal DNA binding domain of Wilms tumor suppressor gene, WT1[5], [6]. Here, EWSR1 is linked to desmoplastic small round cell tumor.