In this way, a diagnosis of proximal-type ES was based on the presence of larger/rhabdoid cells in a tumor, with an otherwise epithelioid morphology, exhibiting a polyphenotypic expression with mesenchymal markers (vimentin, CD34); a myogenic marker (desmin) along with epithelial markers (CK, CK7, EMA). This evidence concerns the gene KRT7 and epithelioid sarcoma.