2)Harmonin: gene site, if mutant, causes DFNB18, and was mapped at chromosome 11 (11p15.1), at the same gene location as USH1C (Usher Syndrome Type IC – 11p15.1).7, 11 Gene USH1C (28 exons) codifies a protein that contains domain PDZ, denominated harmonin. Here, USH1C is linked to Usher syndrome type 1C.